Desmoid tumor of the abdominal wall: Case report

Abstract

Extra-abdominal desmoid tumors are a rare condition caused by fibroblast proliferation and a low mitotic index. Diagnosis is based on clinical history, physical examination, imaging method, cytopathological examination, in addition to immunohistochemistry. This is a case report of a large desmoid tumor located in the abdominal wall of an 18-year-old patient without comorbidities who was admitted to the Hospital Regional do Cariri with complaints of severe abdominal pain, vaginal bleeding, and difficulty in evacuation. The immunohistochemical study revealed nuclear expression for β- catenin, the findings being compatible with desmoid tumor. Surgical treatment consisted of tumor resection with a safe margin. This was followed by closing the abdominal wall defect with a flexible laminated mesh and construction of a neo-umbilicus. There was good recovery. The patient will be monitored to prevent relapses.

Keywords: Aggressive fibromatosis/surgery; abdominal wall; abdominal fibromatosis.